+
 

1. Ϲ
1. , ġ,

A.ġ
  • : ټ : 102510/L
    ٱ : 50 150/7L




    >

    >Ʊ

    >0.41.0%

    >ȣ߱

    >

    >40.050.0%

    >

    >İ

    >ٱ

    >пٱ

    >ȣ걸

    >1.05.0%

    >ȣⱸ

    >00.4%

    >Ʊ

    >Ʊ

    >00.4%

    >ȣ⼺Ʊ

    >14.025.0%

    >ٿƱ

    >Ʊ

    >ٺп

    >00.6%

    >

    >15.025.0%

    >ٱ

    >2.85.4%

    >

    >1.86.4%

    >M/E

    >1.53.3%



    2.̻ġ ̴ ȯ : ޼, ҷ, , Ǽ , Ǽ,
    Gaucher , Niemann-Pick , Hodgkin (, ), ǰҼڹݺ,


2.
  • ()Դϴ. ٺ()κ
    , ܰ踦 ȣ߱, ȣ걸, ȣⱸ, , , ϴ. κ
    ٴ÷ Ͽ Ż, ¸ ϴ ˻Դϴ. ̳ ҷ , ġȿ
    ߿մϴ.